sentence: Long QT syndrome ( LQTS ) , short QT syndrome ( SQTS ) , sick sinus syndrome ( SSS ) , cardiac conduction defect ( CCD ) , BrS , catecholaminergic polymorphic ventricular tachycardia ( CPVT ) , early repolarization syndrome ( ERS ) , and familial Atrial Fibrillation ( AF ) are the presently known cardiac channelopathies , which could occur due to a single or multiple defect in the genes linked to cardiac rhythm generation and propagation.In this review , we will describe exclusively on LQTS linked arrhythmias , its pathophysiology and presently available clinical management .